A Case of Orbital Liposarcoma

Liposarcoma is extremely rare malignant tumor which develops primary in the orbit. Here, we report a case of primary orbital liposarcoma in 17 year old female patient. She visited our hospital due to decreased visual acuity and protrusion of Rt. eyeball. Malignant tumor was suspected by many examination. So exenteration was performed and tumor mass was confirmed as liposarcoma by pathologic examination. She was received cobalt 60 radiation therapy, but recurrent tumor mass appeared at the orbital apex 1 year after operation.

A Case of Congenital Optic Pit

Optic pits are congenital craterlike holes or indentation in the surface of the optic disc. They are oval in shape and located in the inferior temporal quadrant of the optic disc. The authors experienced a case of congenital optic pit of the left eye of 18 year old male-patient. Fluorescein angiography showed hypofluorescence of the pit in early arteriovenous phase, becomming hyperfluorescence in the late phase. Ophthalmoscopic view of the diseased eye showed no abnormality of macular area. There was no visual field defect except the enlarged physiologic blind spot. Here we briefly report a case of congenital optic pit. referring the literature relating to the optic pit.

A Case of Chronic Cyclitis

Since Ernst Fuchs had described the chronic cyclitis as cyclitis in 1892, there have been many reports about the chronic cyclitis with the development of the binocular indirect ophthalmoscope and the Schepens' scleral depressor and gonioscope. The chronic cyclitis comes incidious onset with minimal symptoms of hazy vision and vitreous opacity. The authors experienced a case of chronic cyclitis of the left eye of 33 year old male patient who has been treated with systemic corticosteroid and antihistamines. Here, we briefly report it referring the literature about the chronic cyclitis.

Gronblad-Strandberg Syndrome in Three Consecutive Brother and Sisters

Pseudoxanthoma elasticum is an inherited disease with degenerative changes in elastic tissue of human body. Skin lesion in pseudoxanthoma elasticum is easily understood and histopathologic finding of skin lesion is chracteristic in diagnosis of pseudoxanthoma elasticum. Pseudoxanthoma elasticum combined with the both dermatologic and ocular manifestations is called Gronblad-Strandberg syndrome. Angioid streak appears ophthalmoscopically as a network of red or dark brown streaks mainly around optic disc and may occur alone or in association with various systemic diseases involving pseudoxanthoma elasticum. Fluorescein angiography of fundus is evaluated as a means of detecting early angioid streak or some other ocular manifestations of pseudoxanthoma elasticum which may be observable only by this method and not previously described. To our knowledge, this is the first three cases of Gronblad-Strandberg syndrome in Korean consecutive siblings which are presented with pathologic and fluorescein angiographic studies.

A Case of Malignant Melanoma in the Conjunctiva

Authors repGrted one case of malignant melanoma which is located in the conjunctiva of the left eye This male patient, aged 45, has been a history of progressive enlargement of this melanoma since over ten years. At the time of first visit to the hospital, this melanoma revealed dark brownish strawbery-like pedunclated mass in his medial bulbar conjunctiva, and extended to fornix, palpebral conjunctiva, and lidmargin. Subtotal exenteration, BCG therapy, and X-ray radiation was performed successfully and was conformed histopathologically. In addition to some clinical observation, a brief review of literature has been described.

Therapeutic Effects of Ruby Laser Photocoagulation on Retinal Diseases

I. Central Serous Chorioretinopathies: One hundred and nine patients with central serous retinopathy were an a lysed after treatment with AO Laser Photocoagulator. The patients in this study were mainly male (87%) between the ages of 30 and 40 years (81.5%). Involvement was exclusively unilateral (98.1 %), and fluorescein fundus angiography revealed leaking points in almost all cases (98.1%). Majority of patients (67.4%) recovered normal vision with one or two sittings of photocoagulation, each sitting composed of 6 to 8 energy pulses producing grade I lesion. During the course of this study normal vision is gained in 80.2% of patients. With the development of fluorescein fundus angiography the lesion of central serous retinopathy were found to be choroidal abnormalities associated serous leakage across Bruch's membrane. Burn is made by the light energy delivered to pigment epithlium. The burn results, through normal healing processes, in a scar, which seals off the communication across Bruch's membrane. This phenomenon constructs the basis of treatment of central serous retinopathy with photocoagulation. II. Diabetic Retinopathies: Diabetic retinopathy is rapidly becoming the prominent cause of blindness in the world. The striking change of retinopathy is in the venous side of retinal capillaries and their altered function leads to exudation, hemorrhage, formation of new vessels, and fibrosis over the retinal plane or into vitreous, resuJting ultimately into blindness. Of the 34 patients treated with AO Ruby Photocoagulator at Han Yang Uni. Hos., the response of the patients in pre-proliferative stage was excellent, all of them recovering vision above 0.8. The patients in proliferative stage, however, responded poorly to photocoagulation. It is learned in this study that the optimal time of photocoagulation is in the pre-proliferative stage. The photocoagulation of retinitis proliferans has some effect only in arresting or delaying the progress of retinal changes. III. Focal Choroiditis: Nonsuppurative intracular inflammation is caused by various etiology. Scrutinization such as serologic and skin test or x-ray finding is important for the diagnosis of uveitis but not so significant as the definitive clinical characteristics of specific forms of ocular inflammation. Focal choroiditis, sized less than 1/4 disk diameter, was coagulated with ruby laser. Four out of 6 patients recovered good vision, the lesion being replaced by a scar. The remaining two patients did not visit the hospital after one session of photocoagulation. It is emphasized by the author that the focal choroiditis is excellent indication to the laser photocoagulation. IV. Eales' Disease: Eales' disease is considered to be due to hypersensitivity to mostly tuberculo-antigen, clinically characterized by retinal perivenous exudate, neovascularization and vitreous hemorrhage. A boy has recovered his normal vision after 18 sessions of ruby laser photocoagulation. There have been no benificent effects where photocoagulation was discontinued after two or three sittings.

A Case of Cysticercosis in Lateral Rectus Muscle

The authers have recently experienced a case of cysticercosis in the left lateral rectus muscleof 9 years old Korean boy. The cyst, 3 X 3 X 5mm of size, was located within the muscle sheath and removed surgically in its capsule, confirmed as cysticercosis microscopically. We presents here a report of cysticercosis with a brief review of literature.

A Case of Cysticercosis in Lateral Rectus Muscle

The authers have recently experienced a case of cysticercosis in the left lateral rectus muscleof 9 years old Korean boy. The cyst, 3 X 3 X 5mm of size, was located within the muscle sheath and removed surgically in its capsule, confirmed as cysticercosis microscopically. We presents here a report of cysticercosis with a brief review of literature.

A Case of von Hippel-Lindau Disease

Recently, we have experienced a case of von Hippel-Lindau's disease. The patient was a 16 years old Korean girl who visited to our hospital because of visual impairment in both eyes since childhood, mental retardation, dysarthria and gait disturbance. On the eye examination, visual acuity of both eyes were 0.04, incorrectable, funduscopy revealed optic atrophy and typical angiomatosis retinae in the right eye and optic atrophy associated with retinal detachment in the left eye. The cerebral angiography showed a space occupying mass in the left cerebellum. Thus this case was presented as a complete form of von Hippel-Lindau's disease, and a brief review of literatures was also discussed.

Chromic Cyclitis, Pars Planitis

This disease entity, first described under the desgnation of cyclitis by Ernst Fuchs, has received renewed attention in the recenet years, having been described as peripheral uveitis, pars planitis, and cyclitis with peripheral chorioretinitis. Apparently new ophthalmoscopic findings have caused some obserbers to believe they are dealing with a new entity, because indirect ophthalmoscopy with scleral depression shows exudation in the pars plana region in severe or advanced cases. In this entity, The following characteristic findings are noted, occurring bilaterally, inflammatory cells in anterior vitreous, slight flare and cells in the anterior chamber in come instances, dilated veins, and snowball deposition of inflammatory cells over the pare plana and ora serrata, seen with scleral depression and indirect ophthalmoscope extending over the lower 180 degrees. Cystoid macular degeneration are demonstrated with fluorescein angiography in over half the caces; papilledema may occur in late cases; and peripheral retinal perivascular sheathing is noted in long standing cases.

A Case of Wilson's Disease

The authors have recntly experienced a case of Wilson's disease which was developed Kayser-Fleischer ring. The 13 years old male patient has dysarthria, slurring speech, choreiform movement and gait disturbance about for 2 years. The treatment was performed by B.A.L. and penicillamine and the result has been excellent up to date, 31/2 months after medical treatment. Physical examination on discharge were normal mentality, absence of tremors and pale Kayser Fleischer ring.